Trial Outcomes & Findings for Rituximab to Treat Moderate Aplastic Anemia, Pure Red Cell Aplasia, or Diamond Blackfan Anemia (NCT NCT00229619)

NCT ID: NCT00229619

Last Updated: 2018-09-18

Results Overview

Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses. Primary endpoint will determine immune response by evaluating changes in peripheral blood counts (platelets, absolute neutrophil count, reticulocyte count, hemoglobin) and transfusion requirements at 6 months. The response wil be will be categorized as complete, partial or no response. Subjects will be categorized as complete responders if their blood counts return to normal. Subjects will categorized as partial responders if there is an improvement in 2 or 3 of the depressed baseline blood counts.

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

11 participants

Primary outcome timeframe

6 months

Results posted on

2018-09-18

Participant Flow

Participant milestones

Participant milestones
Measure
Rituximab Treated Subjects
Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses.
Overall Study
STARTED
11
Overall Study
COMPLETED
11
Overall Study
NOT COMPLETED
0

Reasons for withdrawal

Withdrawal data not reported

Baseline Characteristics

Rituximab to Treat Moderate Aplastic Anemia, Pure Red Cell Aplasia, or Diamond Blackfan Anemia

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Rituximab Subjects
n=11 Participants
Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses.
Age, Categorical
<=18 years
0 Participants
n=99 Participants
Age, Categorical
Between 18 and 65 years
11 Participants
n=99 Participants
Age, Categorical
>=65 years
0 Participants
n=99 Participants
Sex: Female, Male
Female
8 Participants
n=99 Participants
Sex: Female, Male
Male
3 Participants
n=99 Participants

PRIMARY outcome

Timeframe: 6 months

Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses. Primary endpoint will determine immune response by evaluating changes in peripheral blood counts (platelets, absolute neutrophil count, reticulocyte count, hemoglobin) and transfusion requirements at 6 months. The response wil be will be categorized as complete, partial or no response. Subjects will be categorized as complete responders if their blood counts return to normal. Subjects will categorized as partial responders if there is an improvement in 2 or 3 of the depressed baseline blood counts.

Outcome measures

Outcome measures
Measure
Rituximab Subjects
n=11 Participants
Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses.
Response to Rituximab
Complete response
0 participants
Response to Rituximab
Partial response
2 participants
Response to Rituximab
No Response
9 participants

SECONDARY outcome

Timeframe: 3 months

Outcome measures

Outcome measures
Measure
Rituximab Subjects
n=11 Participants
Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses.
Response Assessment at 3 Months
Complete response
0 Participants
Response Assessment at 3 Months
Partial response
1 Participants
Response Assessment at 3 Months
No response
10 Participants

SECONDARY outcome

Timeframe: 12 months

Outcome measures

Outcome measures
Measure
Rituximab Subjects
n=11 Participants
Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses.
Response Rates at 12 Months (After the First Dose of Study Med)
Complete response
0 Participants
Response Rates at 12 Months (After the First Dose of Study Med)
Partial response
3 Participants
Response Rates at 12 Months (After the First Dose of Study Med)
Relapse after response
1 Participants
Response Rates at 12 Months (After the First Dose of Study Med)
No response
7 Participants

Adverse Events

Rituximab Subjects

Serious events: 4 serious events
Other events: 4 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Rituximab Subjects
n=11 participants at risk
Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses.
Metabolism and nutrition disorders
Acidosis
9.1%
1/11
Infections and infestations
Infection with normal ANC
9.1%
1/11
Vascular disorders
right popliteal artery occlusion
9.1%
1/11
Infections and infestations
Abdominal abscess
9.1%
1/11
Blood and lymphatic system disorders
anemia
9.1%
1/11
Skin and subcutaneous tissue disorders
skin breakdown
9.1%
1/11
Infections and infestations
Cellulitis
9.1%
1/11

Other adverse events

Other adverse events
Measure
Rituximab Subjects
n=11 participants at risk
Rituximab will be given to moderate aplastic anemia (MAA), pure red cell aplasia or Diamond Blackfan anemia subjects. Rituxmiab will be given to evaluate if these bone marrow failure syndrome subjects will have an immune response to the intervention. The subjects will receive 375 mg/ meters squared of rituximab which will be infused intravenously once evey week for a total of 4 doses.
Blood and lymphatic system disorders
Bleeding
9.1%
1/11
Blood and lymphatic system disorders
Bruising
9.1%
1/11
Respiratory, thoracic and mediastinal disorders
Cough
9.1%
1/11
General disorders
Cytokine release syndrome/ acute infusion reaction
9.1%
1/11
General disorders
Pain
18.2%
2/11
Immune system disorders
Serum sickness
9.1%
1/11
General disorders
Fatigue
9.1%
1/11
Infections and infestations
Urinary Tract Infection
9.1%
1/11
Gastrointestinal disorders
Mouth sores
9.1%
1/11
General disorders
Headache
9.1%
1/11
Cardiac disorders
arrythmia
9.1%
1/11
Cardiac disorders
Mild swelling of extremity
18.2%
2/11
Respiratory, thoracic and mediastinal disorders
Dyspnea on exertion
9.1%
1/11
General disorders
Pallor
9.1%
1/11
Infections and infestations
strep throat
9.1%
1/11
Skin and subcutaneous tissue disorders
dry, flaking skin temporal area
18.2%
2/11
Immune system disorders
Lymph node
9.1%
1/11
Hepatobiliary disorders
urinary frequency/ dysuria
9.1%
1/11
Infections and infestations
infection (Strep viridans)
9.1%
1/11
General disorders
fever
9.1%
1/11
Blood and lymphatic system disorders
neutropenia
9.1%
1/11
Blood and lymphatic system disorders
Decreased hemoglobin
9.1%
1/11
Blood and lymphatic system disorders
Decreased lymphocytes
9.1%
1/11
Blood and lymphatic system disorders
Decreased platelets
9.1%
1/11
Cardiac disorders
Palpitations
9.1%
1/11
Skin and subcutaneous tissue disorders
Right foot ulcer
9.1%
1/11
Gastrointestinal disorders
Gastroenteritis
9.1%
1/11
Gastrointestinal disorders
Splenomegaly
9.1%
1/11
Hepatobiliary disorders
Increased LFTs
9.1%
1/11
Infections and infestations
Upper respiratory tract
9.1%
1/11
General disorders
Arthralgia
9.1%
1/11
General disorders
tooth pain
9.1%
1/11
Skin and subcutaneous tissue disorders
Lip. Pimple
9.1%
1/11

Additional Information

Adrian Wiestner MD, NHLBI

NIH National Heart, Lung and Blood Institute

Phone: 301-594-6855

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place