Trial Outcomes & Findings for Study to Assess the Safety, Tolerability, and Efficacy of Viltolarsen in Ambulant and Non-Ambulant Boys With DMD (Galactic53) (NCT NCT04956289)

NCT ID: NCT04956289

Last Updated: 2024-08-20

Results Overview

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

20 participants

Primary outcome timeframe

baseline to up to 48 weeks of treatment

Results posted on

2024-08-20

Participant Flow

Participants were enrolled in the study from July 1, 2021 to July 22, 2022 at 8 sites in the United States, Italy, Russia, Spain, and China.

A total of 27 participants were screened, but 3 participants did not meet inclusion or exclusion criteria and 4 participants failed to screen for other reasons.

Participant milestones

Participant milestones
Measure
Viltolarsen 80mg/kg
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Overall Study
STARTED
20
Overall Study
Ambulant
10
Overall Study
Non-ambulant
10
Overall Study
COMPLETED
20
Overall Study
NOT COMPLETED
0

Reasons for withdrawal

Withdrawal data not reported

Baseline Characteristics

Study to Assess the Safety, Tolerability, and Efficacy of Viltolarsen in Ambulant and Non-Ambulant Boys With DMD (Galactic53)

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Viltolarsen 80mg/kg
n=20 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Age, Continuous
12.8 years
STANDARD_DEVIATION 5.47 • n=99 Participants
Sex: Female, Male
Female
0 Participants
n=99 Participants
Sex: Female, Male
Male
20 Participants
n=99 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
0 Participants
n=99 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
20 Participants
n=99 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
0 Participants
n=99 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=99 Participants
Race (NIH/OMB)
Asian
5 Participants
n=99 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=99 Participants
Race (NIH/OMB)
Black or African American
0 Participants
n=99 Participants
Race (NIH/OMB)
White
15 Participants
n=99 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=99 Participants
Race (NIH/OMB)
Unknown or Not Reported
0 Participants
n=99 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10).

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=20 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Treatment Emergent Adverse Events
19 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10). Only participants with Treatment-Emergent Adverse Events were evaluated.

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=19 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Treatment Emergent Adverse Events by Maximum Severity
Mild
7 Participants
Number of Participants With Treatment Emergent Adverse Events by Maximum Severity
Moderate
12 Participants
Number of Participants With Treatment Emergent Adverse Events by Maximum Severity
Severe
0 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10). Only participants with Treatment-Emergent Adverse Events were evaluated.

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=19 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Dose not changed
16 Participants
Number of Participants With Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Dose reduced
0 Participants
Number of Participants With Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Drug interrupted
2 Participants
Number of Participants With Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Drug withdrawn
0 Participants
Number of Participants With Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Not applicable
1 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10). Only participants with Investigational Product-related Treatment Emergent Adverse Events were evaluated.

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=19 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Treatment Emergent Adverse Events by Worst Outcome
Recovered or resolved
17 Participants
Number of Participants With Treatment Emergent Adverse Events by Worst Outcome
Recovered or resolved with sequelae
0 Participants
Number of Participants With Treatment Emergent Adverse Events by Worst Outcome
Recovering or resolving
0 Participants
Number of Participants With Treatment Emergent Adverse Events by Worst Outcome
Not recovered or resolved
2 Participants
Number of Participants With Treatment Emergent Adverse Events by Worst Outcome
Fatal
0 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10).

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=20 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events
4 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10). Only participants with Investigational Product-related Treatment Emergent Adverse Events were evaluated.

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=4 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Maximum Severity
Mild
3 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Maximum Severity
Moderate
1 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Maximum Severity
Severe
0 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10). Only participants with Investigational Product-related Treatment Emergent Adverse Events were evaluated.

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=4 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Dose not changed
3 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Dose reduced
0 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Drug interrupted
1 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Highest Intervention Level Regarding Investigational Product
Drug withdrawn
0 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10). Only participants with Investigational Product-related Treatment Emergent Adverse Events were evaluated.

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=4 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Worst Outcome
Recovered or resolved
4 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Worst Outcome
Recovering or resolving
0 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Worst Outcome
Not recovered or resolved
0 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Worst Outcome
Fatal
0 Participants
Number of Participants With Investigational Product-related Treatment Emergent Adverse Events by Worst Outcome
Recovered or resolved with sequelae
0 Participants

PRIMARY outcome

Timeframe: baseline to up to 48 weeks of treatment

Population: The Safety Population consisted of all patients who received at least 1 dose of IP (Investigational Product). This was the primary analysis population for the evaluation of safety. It includes all patients treated with viltolarsen both ambulant (10) and non-ambulant (10).

No statistical analysis was performed for this endpoint. The information has been introduced in the section "Adverse Events".

Outcome measures

Outcome measures
Measure
Viltolarsen 80mg/kg
n=20 Participants
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Number of Participants With Adverse Event of Special Interest
5 Participants

Adverse Events

Viltolarsen 80mg/kg

Serious events: 0 serious events
Other events: 19 other events
Deaths: 0 deaths

Serious adverse events

Adverse event data not reported

Other adverse events

Other adverse events
Measure
Viltolarsen 80mg/kg
n=20 participants at risk
Participants who confirmed DMD with genetic deletions amenable to exon 53 skipping were administered an intravenous infusion of Viltolarsen 80 mg/kg once a week for up to 48 weeks.
Infections and infestations
COVID-19
30.0%
6/20 • Number of events 6 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Infections and infestations
Nasopharyngitis
15.0%
3/20 • Number of events 3 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Infections and infestations
Upper respiratory tract infection
15.0%
3/20 • Number of events 3 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Infections and infestations
Influenza
10.0%
2/20 • Number of events 2 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Infections and infestations
Rhinitis
10.0%
2/20 • Number of events 2 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Infections and infestations
Otitis media
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Infections and infestations
Pharyngitis
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Gastrointestinal disorders
Diarrhoea
25.0%
5/20 • Number of events 13 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Gastrointestinal disorders
Food poisoning
10.0%
2/20 • Number of events 8 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Gastrointestinal disorders
Abdominal pain upper
10.0%
2/20 • Number of events 2 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Gastrointestinal disorders
Toothache
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Gastrointestinal disorders
Vomiting
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Nervous system disorders
Headache
20.0%
4/20 • Number of events 4 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Nervous system disorders
Tension headache
5.0%
1/20 • Number of events 2 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
General disorders
Pyrexia
10.0%
2/20 • Number of events 3 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
General disorders
Gait inability
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
General disorders
Non-cardiac chest pain
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Injury, poisoning and procedural complications
Joint injury
10.0%
2/20 • Number of events 2 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Injury, poisoning and procedural complications
Contusion
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Injury, poisoning and procedural complications
Ligament sprain
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Renal and urinary disorders
Haematuria
20.0%
4/20 • Number of events 6 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Renal and urinary disorders
Nephrolithiasis
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Musculoskeletal and connective tissue disorders
Pain in extremity
10.0%
2/20 • Number of events 2 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Musculoskeletal and connective tissue disorders
Back pain
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Musculoskeletal and connective tissue disorders
Myalgia
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Cardiac disorders
Angina pectoris
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Cardiac disorders
Tachycardia
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Investigations
Protein urine
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Investigations
Urine cytology abnormal
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Respiratory, thoracic and mediastinal disorders
Nasal congestion
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Respiratory, thoracic and mediastinal disorders
Oropharyngeal pain
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Skin and subcutaneous tissue disorders
Blister
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Skin and subcutaneous tissue disorders
Rash
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Immune system disorders
Drug hypersensitivity
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03
Vascular disorders
Hypertension
5.0%
1/20 • Number of events 1 • Up to 48 weeks
Number of participants with Treatment Emergent Adverse Events as assessed by CTCAE v4.03

Additional Information

Medical Affairs

NS Pharma, Inc.

Phone: +1(201) 986-3860

Results disclosure agreements

  • Principal investigator is a sponsor employee The most restrictive relevant agreement on the PI provides that the sponsor can review results communications prior to public release and can embargo communications regarding trial results for a period that is not less than 30 days from the time submitted to the sponsor for review.
  • Publication restrictions are in place

Restriction type: OTHER