Trial Outcomes & Findings for A Study Evaluating the Long-Term Safety of Elexacaftor Combination Therapy (NCT NCT04362761)

NCT ID: NCT04362761

Last Updated: 2023-07-28

Results Overview

Recruitment status

COMPLETED

Study phase

PHASE3

Target enrollment

172 participants

Primary outcome timeframe

From Day 1 up to Week 52

Results posted on

2023-07-28

Participant Flow

The study was conducted in 2 parts, Part A and Part B. Participants from Part A also participated in Part B. The Participant flow was planned to be presented for the overall treatment arm.

Participant milestones

Participant milestones
Measure
ELX/TEZ/IVA
Part A: Participants received elexacaftor (ELX) 200 milligram (mg) once daily (qd)/tezacaftor (TEZ)100 mg qd/ivacaftor (IVA)150 mg every 12 hours (q12h) in the treatment period for 48 weeks. Part B: Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period up to 86 weeks.
Part A (48 Weeks)
STARTED
172
Part A (48 Weeks)
COMPLETED
159
Part A (48 Weeks)
NOT COMPLETED
13
Part B (86 Weeks)
STARTED
50
Part B (86 Weeks)
COMPLETED
0
Part B (86 Weeks)
NOT COMPLETED
50

Reasons for withdrawal

Reasons for withdrawal
Measure
ELX/TEZ/IVA
Part A: Participants received elexacaftor (ELX) 200 milligram (mg) once daily (qd)/tezacaftor (TEZ)100 mg qd/ivacaftor (IVA)150 mg every 12 hours (q12h) in the treatment period for 48 weeks. Part B: Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period up to 86 weeks.
Part A (48 Weeks)
Adverse Event
2
Part A (48 Weeks)
Withdrawal of consent (not due to AE)
4
Part A (48 Weeks)
Commercial drug is available for participant
2
Part A (48 Weeks)
Other
5
Part B (86 Weeks)
Commercial drug is available for participant
46
Part B (86 Weeks)
Other
4

Baseline Characteristics

The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
ELX/TEZ/IVA
n=172 Participants
Part A: Participants received ELX 200 mg qd /TEZ 100 mg qd/IVA 150 mg q12h in the treatment period for 48 weeks. Part B: Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period up to 86 weeks.
Age, Continuous
Part A
27.9 years
STANDARD_DEVIATION 11.4 • n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Age, Continuous
Part B
25.6 years
STANDARD_DEVIATION 12.0 • n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Sex: Female, Male
Part A · Female
87 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Sex: Female, Male
Part A · Male
85 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Sex: Female, Male
Part B · Female
26 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Sex: Female, Male
Part B · Male
24 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · Hispanic or Latino
3 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · Not Hispanic or Latino
167 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · Not collected per local regulations
0 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · Hispanic or Latino
1 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · Not Hispanic or Latino
49 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · Not collected per local regulations
0 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · White
169 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · Black or African American
0 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · Asian
2 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · American Indian or Alaska Native
0 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · Native Hawaiian or Other Pacific Islander
0 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part A · White, Asian
1 Participants
n=172 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · White
50 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · Black or African American
0 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · Asian
0 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · American Indian or Alaska Native
0 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · Native Hawaiian or Other Pacific Islander
0 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.
Race/Ethnicity, Customized
Part B · White, Asian
0 Participants
n=50 Participants • The Baseline data were planned to be presented separately for Part A and Part B. Here "Number Analyzed" signifies participants who were evaluable for the specified part of the study.

PRIMARY outcome

Timeframe: From Day 1 up to Week 52

Population: Safety set included all participants who received at least 1 dose of study drug.

Outcome measures

Outcome measures
Measure
Part A: ELX/TEZ/IVA
n=172 Participants
Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period for 48 weeks.
Part A: Safety and Tolerability as Assessed by Number of Participants With Treatment- Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)
Participants with TEAEs
160 Participants
Part A: Safety and Tolerability as Assessed by Number of Participants With Treatment- Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)
Participants with SAEs
26 Participants

PRIMARY outcome

Timeframe: From Day 1 up to Week 86

Population: Safety Set included all participants who received at least 1 dose of study drug.

Outcome measures

Outcome measures
Measure
Part A: ELX/TEZ/IVA
n=50 Participants
Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period for 48 weeks.
Part B: Safety and Tolerability as Assessed by Number of Participants With Treatment- Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)
Participants with TEAEs
50 Participants
Part B: Safety and Tolerability as Assessed by Number of Participants With Treatment- Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)
Participants with SAEs
8 Participants

Adverse Events

Part A: ELX/TEZ/IVA

Serious events: 26 serious events
Other events: 127 other events
Deaths: 0 deaths

Part B: ELX/TEZ/IVA

Serious events: 8 serious events
Other events: 47 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Part A: ELX/TEZ/IVA
n=172 participants at risk
Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg qd in the treatment period for 48 weeks.
Part B: ELX/TEZ/IVA
n=50 participants at risk
Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg qd in the treatment period up to 86 weeks.
Cardiac disorders
Atrial fibrillation
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Cardiac disorders
Myocardial infarction
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Cardiac disorders
Sinus arrest
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Constipation
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Ileus
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
General disorders
Vascular device occlusion
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Hepatobiliary disorders
Cholecystitis
0.00%
0/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Chronic sinusitis
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Infective pulmonary exacerbation of cystic fibrosis
4.7%
8/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
10.0%
5/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Lower respiratory tract infection
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Pneumonia
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Pneumonia pseudomonal
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Injury, poisoning and procedural complications
Limb traumatic amputation
0.00%
0/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Injury, poisoning and procedural complications
Rib fracture
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Investigations
Alanine aminotransferase increased
1.2%
2/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Investigations
Aspartate aminotransferase increased
1.2%
2/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Investigations
Blood bilirubin increased
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Investigations
Forced expiratory volume decreased
0.00%
0/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Investigations
Gamma-glutamyltransferase increased
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Metabolism and nutrition disorders
Electrolyte imbalance
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Metabolism and nutrition disorders
Hyperglycaemia
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Musculoskeletal and connective tissue disorders
Dupuytren's contracture
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Musculoskeletal and connective tissue disorders
Myalgia
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Nervous system disorders
Headache
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Nervous system disorders
Loss of consciousness
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Nervous system disorders
Seizure
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Psychiatric disorders
Aggression
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Psychiatric disorders
Dissociative disorder
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Renal and urinary disorders
Nephrolithiasis
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Reproductive system and breast disorders
Heavy menstrual bleeding
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Reproductive system and breast disorders
Uterine polyp
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Respiratory, thoracic and mediastinal disorders
Haemoptysis
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Respiratory, thoracic and mediastinal disorders
Nasal polyps
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Respiratory, thoracic and mediastinal disorders
Productive cough
0.00%
0/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Skin and subcutaneous tissue disorders
Erythema nodosum
0.58%
1/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.

Other adverse events

Other adverse events
Measure
Part A: ELX/TEZ/IVA
n=172 participants at risk
Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg qd in the treatment period for 48 weeks.
Part B: ELX/TEZ/IVA
n=50 participants at risk
Participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg qd in the treatment period up to 86 weeks.
Investigations
Alanine aminotransferase increased
5.2%
9/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Investigations
Aspartate aminotransferase increased
6.4%
11/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Investigations
Blood bilirubin increased
6.4%
11/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Abdominal pain
9.3%
16/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
6.0%
3/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Abdominal pain upper
7.0%
12/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
4.0%
2/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Constipation
5.8%
10/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
8.0%
4/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Diarrhoea
7.6%
13/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
4.0%
2/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Gastrooesophageal reflux disease
4.7%
8/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
6.0%
3/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Nausea
5.2%
9/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Gastrointestinal disorders
Vomiting
4.7%
8/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
6.0%
3/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
General disorders
Fatigue
7.6%
13/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
2.0%
1/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
General disorders
Malaise
1.7%
3/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
6.0%
3/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
General disorders
Pyrexia
4.1%
7/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
16.0%
8/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Immune system disorders
Immunisation reaction
0.00%
0/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
14.0%
7/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
COVID-19
1.2%
2/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
34.0%
17/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Infective pulmonary exacerbation of cystic fibrosis
9.9%
17/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
42.0%
21/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Influenza
1.2%
2/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
6.0%
3/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Nasopharyngitis
16.3%
28/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
32.0%
16/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Infections and infestations
Upper respiratory tract infection
5.8%
10/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
22.0%
11/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Injury, poisoning and procedural complications
Procedural pain
1.2%
2/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
6.0%
3/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Injury, poisoning and procedural complications
Vaccination complication
14.0%
24/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Musculoskeletal and connective tissue disorders
Arthralgia
7.0%
12/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
8.0%
4/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Nervous system disorders
Dizziness
6.4%
11/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
0.00%
0/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Nervous system disorders
Headache
24.4%
42/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
20.0%
10/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Respiratory, thoracic and mediastinal disorders
Cough
13.4%
23/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
10.0%
5/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Respiratory, thoracic and mediastinal disorders
Oropharyngeal pain
9.3%
16/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
10.0%
5/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Respiratory, thoracic and mediastinal disorders
Productive cough
2.3%
4/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
12.0%
6/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Respiratory, thoracic and mediastinal disorders
Sputum increased
11.0%
19/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
10.0%
5/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
Skin and subcutaneous tissue disorders
Rash
7.0%
12/172 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.
4.0%
2/50 • Day 1 up to Week 52 for Part A, Day 1 up to Week 86 for Part B
MedDRA 24.0 for Part A and MedDRA 25.1 for Part B.

Additional Information

Medical Monitor

Vertex Pharmaceuticals Incorporated

Phone: 617-341-6777

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place