Trial Outcomes & Findings for Methoxsalen and Extracorporeal Photopheresis (ECP) for the Treatment of Pediatric Participants With Steroid Refractory Acute Graft Versus Host Disease (NCT NCT02524847)

NCT ID: NCT02524847

Last Updated: 2020-09-11

Results Overview

OR using the modified IBMTR Severity Index is defined as complete response (CR) + partial response (PR) as follows: * CR: complete resolution of all signs and symptoms of aGvHD in all evaluable organs without addition of next-line systemic treatment * PR: improvement of 1 stage in 1 or more aGvHD target organs without progression in others and without addition of next-line systemic treatment

Recruitment status

TERMINATED

Study phase

PHASE3

Target enrollment

29 participants

Primary outcome timeframe

4 weeks

Results posted on

2020-09-11

Participant Flow

Participants were recruited by multiple treatment centers in the United States and Europe

Participant milestones

Participant milestones
Measure
Methoxsalen With ECP
Participants receive methoxsalen 20 µg/ml in conjunction with extracorporeal photopheresis (ECP) procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Overall Study
STARTED
29
Overall Study
Completed Treatment Up to Week 12
14
Overall Study
Started Second Line Treatment
5
Overall Study
COMPLETED
15
Overall Study
NOT COMPLETED
14

Reasons for withdrawal

Reasons for withdrawal
Measure
Methoxsalen With ECP
Participants receive methoxsalen 20 µg/ml in conjunction with extracorporeal photopheresis (ECP) procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Overall Study
Adverse Event
4
Overall Study
Unsatisfactory Therapeutic Effect
4
Overall Study
Condition no Longer Requires Treatment
4
Overall Study
Death
1
Overall Study
Reason not Specified
1

Baseline Characteristics

Methoxsalen and Extracorporeal Photopheresis (ECP) for the Treatment of Pediatric Participants With Steroid Refractory Acute Graft Versus Host Disease

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Methoxsalen With ECP
n=29 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Age, Continuous
8.6 years
STANDARD_DEVIATION 5.02 • n=99 Participants
Sex: Female, Male
Female
12 Participants
n=99 Participants
Sex: Female, Male
Male
17 Participants
n=99 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
5 Participants
n=99 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
24 Participants
n=99 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
0 Participants
n=99 Participants
Race/Ethnicity, Customized
Asian
1 Participants
n=99 Participants
Race/Ethnicity, Customized
Black or African American
2 Participants
n=99 Participants
Race/Ethnicity, Customized
White
22 Participants
n=99 Participants
Race/Ethnicity, Customized
Other
4 Participants
n=99 Participants

PRIMARY outcome

Timeframe: 4 weeks

Population: All participants

OR using the modified IBMTR Severity Index is defined as complete response (CR) + partial response (PR) as follows: * CR: complete resolution of all signs and symptoms of aGvHD in all evaluable organs without addition of next-line systemic treatment * PR: improvement of 1 stage in 1 or more aGvHD target organs without progression in others and without addition of next-line systemic treatment

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=29 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Number of Participants Achieving Overall Response (OR) Using the Modified International Bone Marrow Transplant Registry (IBMTR) Severity Index at Week 4
16 Participants

SECONDARY outcome

Timeframe: 16 weeks

Population: All participants

Clinically significant changes in vital signs, laboratory values and investigations are reported as adverse events. Summary data are provided below, with details listed in the adverse events module.

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=29 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Number of Participants With Adverse Events
Death for any cause
3 Participants
Number of Participants With Adverse Events
Any serious AE
12 Participants
Number of Participants With Adverse Events
Non-serious TEAE at 5% threshold
17 Participants

SECONDARY outcome

Timeframe: 8 weeks

Population: Evaluable Participants (Participants with appropriate efficacy data at the given time point)

OR using the modified IBMTR Severity Index is defined as complete response (CR) + partial response (PR) as follows: * CR: complete resolution of all signs and symptoms of aGvHD in all evaluable organs without addition of next-line systemic treatment * PR: improvement of 1 stage in 1 or more aGvHD target organs without progression in others and without addition of next-line systemic treatment

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=19 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Percentage of Participants Achieving Overall Response (OR) Using Modified IBMTR Severity Index at Week 8
73.7 percentage of participants
Interval 48.8 to 90.9

SECONDARY outcome

Timeframe: 12 weeks

Population: Evaluable Participants (Participants with appropriate efficacy data at the given time point)

OR using the modified IBMTR Severity Index is defined as complete response (CR) + partial response (PR) as follows: * CR: complete resolution of all signs and symptoms of aGvHD in all evaluable organs without addition of next-line systemic treatment * PR: improvement of 1 stage in 1 or more aGvHD target organs without progression in others and without addition of next-line systemic treatment

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=14 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Percentage of Participants Achieving Overall Response (OR) Using Modified IBMTR Severity Index at Week 12
78.6 percentage of participants
Interval 49.2 to 95.3

SECONDARY outcome

Timeframe: 16 weeks

Population: Population meeting the criterion

Duration of first response is presented for patients whose disease progressed. Duration of response is defined in the following way: Patients whose response failed: Date at which 1st disease progression occurs - date of 1st response +1. Patients whose response did not relapse: Date of 16 week follow-up or final assessment prior to week 16 (if patient withdrew early) - date of 1st response.

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=18 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Duration of Response (Days) Within 16 Weeks Using Modified IBMTR Severity Index
13.5 days
Interval 4.0 to 50.0

SECONDARY outcome

Timeframe: 4 weeks, 8 weeks, and 12 weeks

Population: All participants with a score at the given time point

ORR is defined as the percentage of patients who achieve an overall response after 4 weeks, 8 weeks, and 12 weeks of ECP treatment according to a scoring algorithm applied to calculate the grade of aGvHD using the modified Glucksberg Criteria.

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=29 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Overall Response Rate (ORR) According to the Modified Glucksberg Criteria
Week 4
50 percentage of participants
Interval 29.1 to 70.9
Overall Response Rate (ORR) According to the Modified Glucksberg Criteria
Week 8
63.2 percentage of participants
Interval 38.4 to 83.7
Overall Response Rate (ORR) According to the Modified Glucksberg Criteria
Week 12
78.6 percentage of participants
Interval 49.2 to 95.3

SECONDARY outcome

Timeframe: From diagnosis of aGvHD to 12 Weeks

Population: All participants

Steroids administered from diagnosis of aGvHD to 12 Weeks after initiation of ECP treatment

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=29 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Cumulative Dose of Daily Steroids
1917 mg
Interval 192.0 to 6895.0

SECONDARY outcome

Timeframe: at 4, 8 and 12 weeks

Population: All participants with scores at the given time point

Number of patients whose skin was rated as Stage 0 - 4 using the modified Glucksberg criteria based on the Graft versus Host Disease (GvHD) rash - Stages are defined as 0=No GvHD rash, 1=Maculopapular rash on \<25% body surface area (BSA), 2=Maculopapular rash on 25-50% BSA, 3=Maculopapular rash on \>50% BSA, and 4=Generalized erythroderma plus bullous formation, which are blisters bigger than 5 mm across

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=29 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 1
5 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 2
1 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 0
9 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 1
8 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 2
3 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 3
3 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 4
0 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 0
11 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 3
1 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 4
0 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 0
10 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 1
2 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 2
1 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 3
1 Participants
Number of Patients With Skin Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 4
0 Participants

SECONDARY outcome

Timeframe: at 4, 8 and 12 weeks

Population: All participants with scores at the given time point

Number of patients whose liver was rated as Stage 0 - 4 on the modified Glucksberg criteria - Stages are based on level of bilirubin, defined as: Stage 0 = Bilirubin \< 2.0 mg/dL, Stage 1 = Bilirubin 2.0-3.0 mg/dL, Stage 2 = Bilirubin 3.1-6.0 mg/dL, Stage 3 = Bilirubin 6.1-15.0 mg/dL, and Stage 4 = Bilirubin \> 15.0 mg/dL

Outcome measures

Outcome measures
Measure
Methoxsalen With ECP
n=29 Participants
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 0
19 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 1
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 1
1 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 2
1 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 3
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 4 · Stage 4
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 0
13 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 1
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 2
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 3
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 8 · Stage 4
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 0
12 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 2
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 3
0 Participants
Number of Patients With Liver Rated as Stage 0 - 4 Using the Modified Glucksberg Criteria
Week 12 · Stage 4
0 Participants

Adverse Events

Methoxsalen With ECP

Serious events: 12 serious events
Other events: 17 other events
Deaths: 3 deaths

Serious adverse events

Serious adverse events
Measure
Methoxsalen With ECP
n=29 participants at risk
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Infections and infestations
Aspergilloma
3.4%
1/29 • Up to 16 weeks
Infections and infestations
Bk virus infection
3.4%
1/29 • Up to 16 weeks
Infections and infestations
Cellulitis
3.4%
1/29 • Up to 16 weeks
Infections and infestations
Cystitis viral
3.4%
1/29 • Up to 16 weeks
Infections and infestations
Cytomegalovirus infection
3.4%
1/29 • Up to 16 weeks
Infections and infestations
Device related infection
3.4%
1/29 • Up to 16 weeks
Infections and infestations
Hepatitis E
3.4%
1/29 • Up to 16 weeks
General disorders
Pyrexia
6.9%
2/29 • Up to 16 weeks
General disorders
General physical health deterioration
3.4%
1/29 • Up to 16 weeks
Immune system disorders
Acute graft versus host disease
6.9%
2/29 • Up to 16 weeks
Immune system disorders
Acute graft versus host disease in intestine
3.4%
1/29 • Up to 16 weeks
Immune system disorders
Acute graft versus host disease in liver
3.4%
1/29 • Up to 16 weeks
Immune system disorders
Graft versus host disease
3.4%
1/29 • Up to 16 weeks
Blood and lymphatic system disorders
Autoimmune haemolytic anaemia
3.4%
1/29 • Up to 16 weeks
Blood and lymphatic system disorders
Pancytopenia
3.4%
1/29 • Up to 16 weeks
Metabolism and nutrition disorders
Hyperkalaemia
3.4%
1/29 • Up to 16 weeks
Metabolism and nutrition disorders
Hypokalaemia
3.4%
1/29 • Up to 16 weeks
Metabolism and nutrition disorders
Hypomagnesaemia
3.4%
1/29 • Up to 16 weeks
Renal and urinary disorders
Cystitis haemorrhagic
3.4%
1/29 • Up to 16 weeks
Renal and urinary disorders
Renal failure
3.4%
1/29 • Up to 16 weeks
Musculoskeletal and connective tissue disorders
Arthralgia
3.4%
1/29 • Up to 16 weeks
Nervous system disorders
Haemorrhage intracranial
3.4%
1/29 • Up to 16 weeks
Respiratory, thoracic and mediastinal disorders
Respiratory failure
3.4%
1/29 • Up to 16 weeks
Vascular disorders
Hypertension
3.4%
1/29 • Up to 16 weeks

Other adverse events

Other adverse events
Measure
Methoxsalen With ECP
n=29 participants at risk
Participants receive methoxsalen 20 µg/ml in conjunction with ECP procedure three times per week for Weeks 1 to 4, and two times per week for Weeks 5 to 12.
Gastrointestinal disorders
Abdominal pain
13.8%
4/29 • Up to 16 weeks
Gastrointestinal disorders
Nausea
13.8%
4/29 • Up to 16 weeks
Metabolism and nutrition disorders
Hyperglycaemia
10.3%
3/29 • Up to 16 weeks
Metabolism and nutrition disorders
Hypocalcaemia
10.3%
3/29 • Up to 16 weeks
Metabolism and nutrition disorders
Hyperkalaemia
6.9%
2/29 • Up to 16 weeks
Metabolism and nutrition disorders
Hypophosphataemia
6.9%
2/29 • Up to 16 weeks
Metabolism and nutrition disorders
Malnutrition
6.9%
2/29 • Up to 16 weeks
Vascular disorders
Hypertension
13.8%
4/29 • Up to 16 weeks
Vascular disorders
Hypotension
10.3%
3/29 • Up to 16 weeks
Infections and infestations
Clostridium difficile infection
6.9%
2/29 • Up to 16 weeks
Infections and infestations
Cytomegalovirus infection
6.9%
2/29 • Up to 16 weeks
Infections and infestations
Pneumonia
6.9%
2/29 • Up to 16 weeks
Respiratory, thoracic and mediastinal disorders
Cough
13.8%
4/29 • Up to 16 weeks
General disorders
Pyrexia
10.3%
3/29 • Up to 16 weeks
Immune system disorders
Hypogammaglobulinaemia
10.3%
3/29 • Up to 16 weeks
Investigations
Immunoglobulins decreased
6.9%
2/29 • Up to 16 weeks
Psychiatric disorders
Depression
6.9%
2/29 • Up to 16 weeks

Additional Information

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Phone: 800-844-2830

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place