Trial Outcomes & Findings for A Study of the Safety and Immunogenicity of Repeated rhC1INH Administration (NCT NCT00851409)

NCT ID: NCT00851409

Last Updated: 2018-06-26

Results Overview

Prior to the treatment period, patients enrolled in the study, were asked about the amount of "HAE" attacks in the past 2 years, (calculated to attacks/week), this number is defined as "Historical". During the treatment period, patients received a dose of 50 IU/kg of "rhC1INH" administered by slow "IV" injection over 4 to 5 minutes, once a week during an eight week period. The amount of attacks during this period is defined as "Prophylaxis" (calculated to attacks/week).

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

25 participants

Primary outcome timeframe

8 weeks

Results posted on

2018-06-26

Participant Flow

Patients with a history of frequent attacks, defined as "HAE" attacks occurring at least every two weeks were included in the study.

Participant milestones

Participant milestones
Measure
Recombinant Human C1 Inhibitor
Weekly administration of 50 IU/kg recombinant human C1 inhibitor Recombinant Human C1 Inhibitor : 50 IU/kg "rhC1INH", "IV" injection over 4 to 5 minutes, once weekly over an 8-week treatment period.
Overall Study
STARTED
25
Overall Study
COMPLETED
25
Overall Study
NOT COMPLETED
0

Reasons for withdrawal

Withdrawal data not reported

Baseline Characteristics

A Study of the Safety and Immunogenicity of Repeated rhC1INH Administration

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Recombinant Human C1 Inhibitor
n=25 Participants
Weekly administration of 50 IU/kg recombinant human C1 inhibitor Recombinant Human C1 Inhibitor : 50 IU/kg "rhC1INH", "IV" injection over 4 to 5 minutes, once weekly over an 8-week treatment period.
Age, Categorical
<=18 years
0 Participants
n=99 Participants
Age, Categorical
Between 18 and 65 years
25 Participants
n=99 Participants
Age, Categorical
>=65 years
0 Participants
n=99 Participants
Sex: Female, Male
Female
20 Participants
n=99 Participants
Sex: Female, Male
Male
5 Participants
n=99 Participants

PRIMARY outcome

Timeframe: 8 weeks

Prior to the treatment period, patients enrolled in the study, were asked about the amount of "HAE" attacks in the past 2 years, (calculated to attacks/week), this number is defined as "Historical". During the treatment period, patients received a dose of 50 IU/kg of "rhC1INH" administered by slow "IV" injection over 4 to 5 minutes, once a week during an eight week period. The amount of attacks during this period is defined as "Prophylaxis" (calculated to attacks/week).

Outcome measures

Outcome measures
Measure
Recombinant Human C1 Inhibitor
n=25 Participants
Recombinant Human C1 Inhibitor : 50 IU/kg "rhC1INH", "IV" injection over 4 to 5 minutes, once weekly over an 8-week treatment period.
HAE Attacks/Week
Historical
0.9 attacks/week
Interval 0.51 to 1.3
HAE Attacks/Week
Prophylaxis
0.4 attacks/week
Interval 0.27 to 0.56

SECONDARY outcome

Timeframe: 8 weeks

"PK/PD" parameters will be based on concentration time curves after the 1st and 8th "rhC1INH" administration.(ratio visit 8/ visit 1, based on the area under the curve from baseline up to 4 hours after administration (AUC 0-4)

Outcome measures

Outcome measures
Measure
Recombinant Human C1 Inhibitor
n=25 Participants
Recombinant Human C1 Inhibitor : 50 IU/kg "rhC1INH", "IV" injection over 4 to 5 minutes, once weekly over an 8-week treatment period.
The Evaluation of Pharmacokinetic/ Pharmacodynamic ("PK/PD")Parameters.
Functional C1 Inhibitor level
1.06 ratio
Interval 0.98 to 1.14
The Evaluation of Pharmacokinetic/ Pharmacodynamic ("PK/PD")Parameters.
Antigenic C1 Inhibitor level
1.02 ratio
Interval 0.91 to 1.15
The Evaluation of Pharmacokinetic/ Pharmacodynamic ("PK/PD")Parameters.
C4 level
1.00 ratio
Interval 0.74 to 1.33

Adverse Events

Recombinant Human C1 Inhibitor

Serious events: 2 serious events
Other events: 2 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Recombinant Human C1 Inhibitor
n=25 participants at risk
Weekly administration of 50 IU/kg recombinant human C1 inhibitor Recombinant Human C1 Inhibitor : 50 IU/kg "rhC1INH", "IV" injection over 4 to 5 minutes, once weekly over an 8-week treatment period.
Infections and infestations
Appendicitis
4.0%
1/25 • Number of events 1 • Treatment emergent adverse events ("TEAEs") were defined as events with start from onset of study drug administration. All Serious Adverse Events("SAEs")are listed.
All Adverse Events ("AEs")occurring within 7 days of onset after study drug administration have been listed.
Respiratory, thoracic and mediastinal disorders
Laryngeal edema
4.0%
1/25 • Number of events 1 • Treatment emergent adverse events ("TEAEs") were defined as events with start from onset of study drug administration. All Serious Adverse Events("SAEs")are listed.
All Adverse Events ("AEs")occurring within 7 days of onset after study drug administration have been listed.

Other adverse events

Other adverse events
Measure
Recombinant Human C1 Inhibitor
n=25 participants at risk
Weekly administration of 50 IU/kg recombinant human C1 inhibitor Recombinant Human C1 Inhibitor : 50 IU/kg "rhC1INH", "IV" injection over 4 to 5 minutes, once weekly over an 8-week treatment period.
Blood and lymphatic system disorders
Anaemia-mild
4.0%
1/25 • Number of events 1 • Treatment emergent adverse events ("TEAEs") were defined as events with start from onset of study drug administration. All Serious Adverse Events("SAEs")are listed.
All Adverse Events ("AEs")occurring within 7 days of onset after study drug administration have been listed.
Blood and lymphatic system disorders
Anaemia-moderate
4.0%
1/25 • Number of events 1 • Treatment emergent adverse events ("TEAEs") were defined as events with start from onset of study drug administration. All Serious Adverse Events("SAEs")are listed.
All Adverse Events ("AEs")occurring within 7 days of onset after study drug administration have been listed.

Additional Information

Medical Affairs Department

Pharming Technologies BV

Phone: +31715247400

Results disclosure agreements

  • Principal investigator is a sponsor employee The investigator must provide a copy of any results communication to the sponsor for review at least 30 days prior to its submission or disclosure. The sponsor may request to delete information identified by sponsor as confidential information prior to submitting such manuscript and/or abstract for publication. For a multi-center study, the investigator must wait (i) at least 24 months after the study is completed at all sites or (ii) until after the multi-center publication.
  • Publication restrictions are in place

Restriction type: OTHER