Trial Outcomes & Findings for Efficacy Study of DX-88 (Ecallantide) to Treat Acute Attacks of Hereditary Angioedema (HAE) (NCT NCT00457015)

NCT ID: NCT00457015

Last Updated: 2021-06-08

Results Overview

The Mean Symptom Complex Severity (MSCS) score is a validated, comprehensive point-in-time measure of symptom severity. At baseline and 4 hours, patients rated the severity on a categorical scale (0 = normal, 1 = mild, 2 = moderate, 3 = severe) for symptoms at each affected anatomical location. Ratings were averaged to obtain the MSCS score. A decrease in MSCS score reflected an improvement in symptoms; clinically meaningful improvement was indicated by a reduction in the score of 0.30 or more.

Recruitment status

COMPLETED

Study phase

PHASE3

Target enrollment

96 participants

Primary outcome timeframe

baseline, 4 hours post-dose

Results posted on

2021-06-08

Participant Flow

Patients were screened in advance of presenting with an HAE attack but were randomized only upon attack.

Participant milestones

Participant milestones
Measure
KALBITOR (Ecallantide)
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Overall Study
STARTED
48
48
Overall Study
COMPLETED
48
47
Overall Study
NOT COMPLETED
0
1

Reasons for withdrawal

Reasons for withdrawal
Measure
KALBITOR (Ecallantide)
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Overall Study
Left study site against medical advice
0
1

Baseline Characteristics

Efficacy Study of DX-88 (Ecallantide) to Treat Acute Attacks of Hereditary Angioedema (HAE)

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
KALBITOR (Ecallantide)
n=48 Participants
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=48 Participants
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Total
n=96 Participants
Total of all reporting groups
Age, Continuous
37.0 years
STANDARD_DEVIATION 13.12 • n=99 Participants
38.0 years
STANDARD_DEVIATION 12.19 • n=107 Participants
37.5 years
STANDARD_DEVIATION 12.61 • n=206 Participants
Sex: Female, Male
Female
37 Participants
n=99 Participants
28 Participants
n=107 Participants
65 Participants
n=206 Participants
Sex: Female, Male
Male
11 Participants
n=99 Participants
20 Participants
n=107 Participants
31 Participants
n=206 Participants
Region of Enrollment
United States
47 Participants
n=99 Participants
48 Participants
n=107 Participants
95 Participants
n=206 Participants
Region of Enrollment
Canada
1 Participants
n=99 Participants
0 Participants
n=107 Participants
1 Participants
n=206 Participants
Symptom Complexes at Baseline
Internal Head/Neck
8 symptom complexes
n=99 Participants
13 symptom complexes
n=107 Participants
21 symptom complexes
n=206 Participants
Symptom Complexes at Baseline
Stomach/GI
18 symptom complexes
n=99 Participants
27 symptom complexes
n=107 Participants
45 symptom complexes
n=206 Participants
Symptom Complexes at Baseline
Genital/Buttocks
6 symptom complexes
n=99 Participants
5 symptom complexes
n=107 Participants
11 symptom complexes
n=206 Participants
Symptom Complexes at Baseline
External Head/Neck
14 symptom complexes
n=99 Participants
9 symptom complexes
n=107 Participants
23 symptom complexes
n=206 Participants
Symptom Complexes at Baseline
Cutaneous
34 symptom complexes
n=99 Participants
21 symptom complexes
n=107 Participants
55 symptom complexes
n=206 Participants

PRIMARY outcome

Timeframe: baseline, 4 hours post-dose

Population: Patients were excluded from the analysis if they did not have data for the endpoint being analyzed. Reasons for patients being excluded are for ecallantide: 1 patient treated for severe upper airway compromise; for placebo: 3 patient treated for severe upper airway compromise and 3 patients with missing 4-hour data. Best score=0.0; worst score=3.0.

The Mean Symptom Complex Severity (MSCS) score is a validated, comprehensive point-in-time measure of symptom severity. At baseline and 4 hours, patients rated the severity on a categorical scale (0 = normal, 1 = mild, 2 = moderate, 3 = severe) for symptoms at each affected anatomical location. Ratings were averaged to obtain the MSCS score. A decrease in MSCS score reflected an improvement in symptoms; clinically meaningful improvement was indicated by a reduction in the score of 0.30 or more.

Outcome measures

Outcome measures
Measure
KALBITOR (Ecallantide)
n=47 Participants
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=42 Participants
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Change From Baseline in Mean Symptom Complex Severity (MSCS) Score at 4 Hours Post-dose
MSCS Score at baseline
2.2 units on a scale
Standard Deviation 0.50
2.0 units on a scale
Standard Deviation 0.35
Change From Baseline in Mean Symptom Complex Severity (MSCS) Score at 4 Hours Post-dose
MSCS Score at 4 hours post-dose
1.4 units on a scale
Standard Deviation 0.75
1.6 units on a scale
Standard Deviation 0.77
Change From Baseline in Mean Symptom Complex Severity (MSCS) Score at 4 Hours Post-dose
Change from baseline in MSCS at 4 hours post-dose
-0.8 units on a scale
Standard Deviation 0.63
-0.4 units on a scale
Standard Deviation 0.82

SECONDARY outcome

Timeframe: 4 hours post-dose

Population: Patients were excluded from this analysis if they did not have data for the endpoint being analyzed. The reasons for patients being excluded from this analysis are for ecallantide: 1 patient treated for severe upper airway compromise and for placebo: 3 patient treated for severe upper airway compromise and 3 patients with missing 4-hour data.

Treatment Outcome Score (TOS) is a validated, comprehensive measure of symptom response to treatment. At 4 hours , patient assessment of response characterized by their change from baseline in symptom severity and collected by anatomic site of attack involvement, was recorded on a categorical scale (significant improvement \[100; best value\]to significant worsening \[-100; worst value\]). Clinically meaningful improvement was indicated by a TOS of 30 or higher.

Outcome measures

Outcome measures
Measure
KALBITOR (Ecallantide)
n=47 Participants
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=42 Participants
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Treatment Outcome Score at 4 Hours Post-Dose
53.4 units on a scale
Standard Deviation 49.70
8.1 units on a scale
Standard Deviation 63.18

SECONDARY outcome

Timeframe: 4 hours post-dose

Population: The time to significant improvement is not provided in this display as the estimated median times were not reached by 240 minutes. Instead, the number of patients with significant improvement is provided per treatment arm.

Patients were to be asked to perform an overall response assessment at intervals during the first 4 hours post-dose. Assessments were to be made relative to baseline (ie, immediately before initial dosing) using a 5-category scale. Categories were: significant improvement = "a lot better or resolved"; improvement = "a little better"; same = response unchanged; worsening = "a little worse"; significant worsening = "a lot worse". Significant improvement is the first time that a patient responded to the overall response assessment as "a lot better or resolved."

Outcome measures

Outcome measures
Measure
KALBITOR (Ecallantide)
n=48 Participants
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=48 Participants
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Patients With Significant Improvement in Overall Response
22 participants
12 participants

SECONDARY outcome

Timeframe: baseline, 4 hours post-dosing

Population: Diary information was not available for 1 patient in the placebo arm. This patient was considered not evaluable and excluded from the analysis.

A successful response was defined as improvement in existing laryngeal symptom complex,stabilization of an existing peripheral symptom complex, or a change from baseline in the MSCS score at 4 hours of at least -1.0.

Outcome measures

Outcome measures
Measure
KALBITOR (Ecallantide)
n=48 Participants
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=47 Participants
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Patients With a Successful Response at 4 Hours Post-dosing, Based on the Change From Baseline in the MSCS Score
45 participants
28 participants

SECONDARY outcome

Timeframe: 24 hours post-dosing

Population: Diary information was not available for 1 patient in the placebo arm. This patient was considered not evaluable and excluded from the analysis.

Maintenance of significant improvement was defined as achieving and maintaining a significant improvement in overall response through 24 hours after dosing. Patient response categories were: significant improvement = "a lot better or resolved"; improvement = "a little better"; same = response unchanged; worsening = "a little worse"; significant worsening = "a lot worse".

Outcome measures

Outcome measures
Measure
KALBITOR (Ecallantide)
n=48 Participants
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=47 Participants
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Proportion of Patients Maintaining a Significant Improvement in Overall Response Through 24 Hours
21 participants
10 participants

Adverse Events

KALBITOR (Ecallantide)

Serious events: 0 serious events
Other events: 5 other events
Deaths: 0 deaths

Placebo

Serious events: 3 serious events
Other events: 9 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
KALBITOR (Ecallantide)
n=48 participants at risk
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=48 participants at risk
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Congenital, familial and genetic disorders
Hereditary angioedema
0.00%
0/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
6.2%
3/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.

Other adverse events

Other adverse events
Measure
KALBITOR (Ecallantide)
n=48 participants at risk
KALBITOR (ecallantide, DX-88) 30 mg given as three 10 mg/mL subcutaneous injections.
Placebo
n=48 participants at risk
Placebo, Phosphate Buffer Saline (PBS), pH 7.0 given as 3 subcutaneous injections.
Gastrointestinal disorders
Diarrhoea
0.00%
0/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
6.2%
3/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
Nervous system disorders
Headache
4.2%
2/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
10.4%
5/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
Gastrointestinal disorders
Nausea
6.2%
3/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
2.1%
1/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
Gastrointestinal disorders
Vomiting
0.00%
0/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.
6.2%
3/48 • up to 7 days post-dose
For patients that were given an open-label dose of ecallantide for severe upper airway compromise or failed or incomplete response, or relapse, all adverse events occurring prior to open-label dosing are included in the following tables where all patients are presented in the double-blind, randomized treatment groups.

Additional Information

Study Director

Shire

Phone: +1 866 842 5335

Results disclosure agreements

  • Principal investigator is a sponsor employee Dyax agreements vary, but Dyax will not prohibit any investigator from publishing. Dyax reviews publications prior to public release and can request deferral by up to 60 days beyond the proposed publication date if necessary to preserve its intellectual property. Dyax can request changes to publications to remove non-study-related confidential information. Dyax can also request deferral of single-center publications until after disclosure of the clinical trial's primary publication.
  • Publication restrictions are in place

Restriction type: OTHER